Impact of SARS-CoV-2 infection and COVID-19 on patients with inborn errors of immunity선천 면역 결함 환자에서 SARS-CoV-2 감염 및 COVID-19의 영향Review Published on 2023-04-012023-07-11 Journal: The Journal of Allergy and Clinical Immunology [Category] COVID19(2023년), [키워드] COVID-19 Cytokine storm immune dysregulation inborn errors of immunity primary immune deficiencies SARS-CoV-2 Type I IFN signaling [DOI] 10.1016/j.jaci.2022.11.010 PMC 바로가기 [Article Type] Review
COVID-19 Vaccination Responses with Different Vaccine Platforms in Patients with Inborn Errors of ImmunityArticle Published on 2023-02-012023-07-10 Journal: Journal of Clinical Immunology [Category] COVID19(2023년), [키워드] Antibody Response COVID-19 inborn errors of immunity SARS-CoV-2 T cell response vaccination [DOI] 10.1007/s10875-022-01382-7 PMC 바로가기
Genetic and immunologic evaluation of children with inborn errors of immunity and severe or critical COVID-19Article Published on 2022-11-012022-11-15 Journal: The Journal of Allergy and Clinical Immunology [Category] SARS, 진단, 치료기술, [키워드] acute respiratory syndrome Affect antibodies Asymptomatic autoantibody B-cell function children children with COVID-19 complement Complication complications coronavirus coronavirus disease COVID-19 COVID-19 complications COVID-19 disease Critical detectable develop diagnosed Diagnostic Criteria died disease evaluated Genetic genetic cause genetic diagnosis help hypoxemic IFN signaling IFN-I immune immune response Immunity immunodeficiency Inborn error inborn errors of immunity individual infected with SARS-CoV-2 Infection Inflammasome Inflammatory Inflammatory factor Mild Molecular diagnosis Mortality mortality rate MOST multisystem inflammatory syndrome in children (MIS-C) Mutation Neutralizing Patient patients patients with asymptomatic Pediatric patients plasma Pneumonia Primary Immunodeficiency reported SARS-CoV-2 SARS-CoV-2-specific antibodies severe COVID-19 disease syndrome tested Treatment Type I IFN was performed were measured whole-exome sequencing [DOI] 10.1016/j.jaci.2022.09.005 PMC 바로가기
COVID-19-related health outcomes in people with primary immunodeficiency: A systematic reviewReview article Published on 2022-10-012022-10-05 Journal: Clinical immunology (Orlando, Fla.) [Category] COVID19(2023년), SARS, 변종, 진단, [키워드] addition approach article association B-cell calculated candidate COVID-19 COVID-19 vaccination duplicates Effectiveness eligible English Factors Fatality rate first positive General population Genetic variant Health Hospitalization illnesses immune response immune system immunodeficiency implication inborn errors of immunity include indicated infections isolate likelihood morbidity and mortality negative test outcome oxygen supplementation pathway performed positive Primary Immunodeficiency Prolonged infection Prophylaxis public health reported response SARS-CoV-2 SARS-CoV-2 test SARS-CoV2 Sequencing Symptom systematic review tested Transmission Vaccinations Vaccine variants whole genome X-linked agammaglobulinemia XLA [DOI] 10.1016/j.clim.2022.109097 [Article Type] Review article
Outcomes following SARS-CoV-2 infection in patients with primary and secondary immunodeficiency in the UKArticle Published on 2022-09-292022-11-15 Journal: Clinical and experimental immunology [Category] SARS, 진단, [키워드] access age anti-SARS-CoV-2 baseline co-morbidity Cohort Combination convalescent plasma COVID-19 COVID-19 treatment CVID demonstrated Dexamethasone died Fatality rate General population high risk hospital Hypogammaglobulinemia IFR immunodeficiency inborn errors of immunity increased the risk Increasing individual Infection Lymphocyte count lymphopenia monotherapy Mortality network outcome overall mortality Patient PID Primary immunodeficiencies receiving REGN-CoV2 Remdesivir reported risk factor SARS-CoV-2 SARS-COV-2 infection secondary immunodeficiencies. therapeutic Tocilizumab Treatment United Kingdom [DOI] 10.1093/cei/uxac008 PMC 바로가기
Impact of vaccination on hospitalization and mortality from COVID-19 in patients with primary and secondary immunodeficiency: The United Kingdom experienceArticle Published on 2022-09-232022-11-15 Journal: Frontiers in Immunology [Category] SARS, 변종, 진단, 치료기술, 치료제, [키워드] Antiviral B.1.1.529 changed cohorts cohorts of patient COVID-19 COVID-19 in patient CVID dominant early stage elevated Fatality rate General population Hospitalization immunodeficiency immunodeficient patient Impact improvement inborn errors of immunity individual Intervention monoclonal antibody morbidity and mortality Mortality MOST naïve nasopharynx omicron outcome pandemic Patient patients PCR PID Primary Immunodeficiency reduced risk SARS-CoV-2 SARS-COV-2 infection SARS-CoV-2 vaccine secondary immunodeficiency serological response severe COVID-19 shown significantly significantly increased the SARS-CoV-2 Treatment treatment strategy United Kingdom vaccination vaccine dose variant Viral detection viral variant widespread [DOI] 10.3389/fimmu.2022.984376 PMC 바로가기
COVID-19 in unvaccinated patients with inborn errors of immunity-polish experienceArticle Published on 2022-09-232022-11-15 Journal: Frontiers in Immunology [Category] SARS, 치료제, [키워드] accounted Adult patient Adults Analysis anti-SARS-CoV-2 Antibiotic therapy antibody-based therapy Antiviral children Comorbidity Complication coronavirus 2 Course COVID-19 COVID-19 symptoms COVID-19 unvaccinated patients death rate deficiency demonstrated diagnosed group high risk humoral immune Immunity immunodeficiency inborn errors of immunity Inflammatory occurred pandemic Patient patients pediatric Prophylaxis reported required respiratory Retrospective study SARS-CoV-2 Severe infection significantly more study group symptomatic syndrome systemic the disease the study group therapy vaccination was used X-linked agammaglobulinemia [DOI] 10.3389/fimmu.2022.953700 PMC 바로가기
Safety and immunogenicity of 3 doses of BNT162b2 and CoronaVac in children and adults with inborn errors of immunityArticle Published on 2022-09-202022-11-15 Journal: Frontiers in Immunology [Category] SARS, 진단, 치료기술, [키워드] age Antibody Response BNT162b2 children CoronaVac COVID-19 determine dose flow cytometry homologous Hong Kong humoral IgG IgG response Immunity immunodeficiency inactivated Inadequate inborn errors of immunity include intracellular cytokine staining Intradermal intramuscular mRNA vaccine neutralization nonrandomized of BNT162b2 omicron Patient patients receiving response S-RBD Safety SARS-CoV-2 antigen T cell response Two patient vaccination Vaccine Virus neutralization [DOI] 10.3389/fimmu.2022.982155 PMC 바로가기
SARS-CoV-2 infection and treatment in a cohort of patients with inborn errors of immunityArticle Published on 2022-08-012022-11-15 Journal: Pediatric allergy and immunology : official public [Category] SARS, 진단, [키워드] Abstract Antiviral antiviral drugs cohort of patient COVID-19 Immunity inborn errors of immunity monoclonal monoclonal antibodies Primary immunodeficiencies SARS-COV-2 infection SARS-CoV2 Treatment [DOI] 10.1111/pai.13833 PMC 바로가기
Real-life data on monoclonal antibodies and antiviral drugs in Italian inborn errors of immunity patients during COVID-19 pandemic코로나19 팬데믹 기간 동안 이탈리아 선천성 면역질환 환자의 단클론항체 및 항바이러스제 실생활 데이터Article Published on 2022-07-282022-09-11 Journal: Frontiers in Immunology [Category] COVID19(2023년), SARS, 진단, 치료제, [키워드] Alpha Analysis Antiviral antiviral agent Antiviral agents antiviral drug antiviral drugs Asymptomatic Care circulating Cohort contributed Course COVID-19 COVID-19 pandemic COVID-19 severity disease disease severity duration of viral shedding Effect Efficacy error evaluated Hospital admission Hospitalization hospitalization-risk hospitalizations hospitalized patients ICU admission Immunity immunized Inborn Inborn errors inborn errors of immunity Infection Italian longitudinal lower risk mAbs mitigate monoclonal monoclonal antibodies monoclonal antibody Mortality mRNA vaccine mRNA vaccines offered Patient patients treated performed positive Prevent prophylactic measure prophylactic measures Re-infection Re-infections reduce reduced Reinfection reported respond risk Safe SARS-CoV-2 SARS-CoV-2 infected patients SARS-CoV-2 positivity SARS-CoV-2 strains SARS-CoV-2 virus severe COVID-19 severe disease Spectrum Spread Strains therapeutic therapy treated vaccination Vaccinations Viral viral shedding viral strain viral strains widespread [DOI] 10.3389/fimmu.2022.947174 PMC 바로가기 [Article Type] Article