Janus kinase inhibitor, tofacitinib, in refractory juvenile dermatomyositis: a retrospective multi-central study in Chinaarticle Published on 2023-10-182024-09-02 Journal: Arthritis Research & Therapy [Category] 대상포진, [키워드] Biologic therapy Janus kinase inhibitor juvenile dermatomyositis refractory Tofacitinib [DOI] 10.1186/s13075-023-03170-z PMC 바로가기 [Article Type] article
Impact of SARS-CoV-2 on the clinical presentation of juvenile idiopathic inflammatory myopathiesarticle Published on 2023-08-112024-09-05 Journal: Pediatric Rheumatology Online Journal [Category] update2024, [키워드] COVID-19 juvenile dermatomyositis Juvenile idiopathic inflammatory myopathies Juvenile overlap myositis Juvenile polymyositis SARS-CoV-2 [DOI] 10.1186/s12969-023-00861-4 PMC 바로가기 [Article Type] article
Updates on Interferon in Juvenile Dermatomyositis: Pathogenesis and TherapyArticle Published on 2021-09-152024-09-04 Journal: Current opinion in rheumatology [Category] 대상포진, [키워드] Biomarker interferon Interferonopathy Janus kinase inhibitor juvenile dermatomyositis Pathogenesis [DOI] 10.1097/BOR.0000000000000816 PMC 바로가기 [Article Type] Article
Favorable outcomes with reduced steroid use in juvenile dermatomyositisResearch Article Published on 2021-08-172024-09-02 Journal: Pediatric Rheumatology Online Journal [Category] 대상포진, [키워드] Biologic therapy Calcinosis Glucocorticoids juvenile dermatomyositis Pediatric rheumatology [DOI] 10.1186/s12969-021-00615-0 PMC 바로가기 [Article Type] Research Article
Fatal outcome of anti-MDA5 juvenile dermatomyositis in a paediatric COVID-19 patient: a case report소아 코로나19 환자에서 발생한 항MDA5 소아 피부근염의 치명적 결과: 증례 보고Case Reports Published on 2021-01-012022-09-11 Journal: Modern rheumatology case reports [Category] 진단, 치료제, [키워드] addition Admission Anti-MDA5 BAL BAS Bronchoalveolar lavage Case report children COVID-19 Cyclophosphamide dermatomyositis diagnosed died disease drug emphysema health condition hemophagocytic lymphohistiocytosis high mortality rate high risk hospital hypoxemic Hypoxemic respiratory failure Immunoglobulin immunosuppressive immunosuppressive therapy Infection initiated Intensive Interstitial lung disease interstitial lung disease (ILD) intravenous Intravenous immunoglobulin juvenile dermatomyositis Lung disease MDA5 Methylprednisolone outcome Patient performed Pneumomediastinum Pneumothorax poor prognosis positive Real-time PCR real-time RT-PCR referred to Respiratory failure risk risk for disease SARS-CoV-2 SARS-COV-2 infection secondary hemophagocytic lymphohistiocytosis Septic shock severe complications subcutaneous emphysema sulfamethoxazole therapy Tofacitinib Treatment worsening [DOI] 10.1080/24725625.2020.1832755 PMC 바로가기 [Article Type] Case Reports
Varicella vaccination elicits a humoral and cellular response in children with rheumatic diseases using immune suppressive treatmentArticle Published on 2017-05-152023-06-02 Journal: Vaccine [Category] 두창, 홍역, [키워드] immunogenicity juvenile dermatomyositis juvenile idiopathic arthritis Juvenile systemic scleroderma Live-attenuated vaccination varicella [DOI] 10.1016/j.vaccine.2017.04.015
Beyond the MHC: A canine model of dermatomyositis shows a complex pattern of genetic risk involving novel lociMHC 너머: 피부근염의 송곳니 모델은 새로운 유전자좌와 관련된 유전적 위험의 복잡한 패턴을 보여줍니다Research Article Published on 2017-02-032022-09-06 Journal: PLoS Genetics [Category] Communicable Disease, [키워드] affected age of onset alleles allelic combination animal model artificial selection association Autoimmune disease biological samples canine chromosome chromosomes Combination complex complex disease complex diseases components conducted conserved conserved regions contribute correlated dermatomyositis disease disease pathogenesis Disease progression disease risk driven by dysfunction encoding Evidence explain exploration Frequency gene-gene interaction Genetic genetic interactions genetic risk genetic risk factor genetic study Genome Genome-wide association studies Genome-wide association study Genotype genotype-phenotype correlation genotypic genotyping Haplotype haplotypes healthy heterogeneity high risk highlight homozygosity human populations identify immunological impacted incidence independent independent of indicated Inflammatory inflammatory disease influences Interaction inverse correlation investigated involved Isolation juvenile dermatomyositis loci major histocompatibility complex MAP3K7CL mapping MHC moderate muscle Myopathy nine PAN2 pattern Phenotypes polymorphism Probability provided Region risk risk allele skin subjects susceptibility susceptibility loci target targets the major histocompatibility thought unique utility Vasculopathy whole genome [DOI] 10.1371/journal.pgen.1006604 PMC 바로가기 [Article Type] Research Article
Update in juvenile myositisarticle Published on 2013-11-252024-09-02 Journal: Current opinion in rheumatology [Category] 대상포진, [키워드] autoantibodies B-cell depletion juvenile dermatomyositis [DOI] 10.1097/01.bor.0000434674.62644.02 PMC 바로가기 [Article Type] article